A polymorphous low-grade adenocarcinoma arising from a minor salivary gland is a rare malignancy of the aerodigestive system. Most such adeno-carcinomas develop in the hard palate. Surgical excision constitutes adequate treatment. A 41-year-old male presented with a mass 1 × 0.7 cm in size at the left side of the tongue near the papilla circumvallata and underwent total resection and primary closure. The pathological diagnosis was a low-grade polymorphous adenocarcarcinoma and the surgical margins were negative. We present the case and review the management of low-grade polymorphous adenocarcinomas of (usually) the hard palate as described in the literature; such tumours are rarely encountered.