Alkaptonuria is a rare autosomal recessive disorder which causes degenerative changes in cartilage, intervertebral disc and other tissues. Although intervertebral disc degeneration is common in alkaptonuria; where there are only a few patients treated surgically for lumbar disc disease.

Diagnosis of alkaptonuria after black colored lumbar discectomy material is a rare condition. We present a case of alkaptonuria, in which the patient was diagnosed after lumbar discectomy.