Familial adenomatous polyposis (FAP) is a rare hereditary syndrome of colon. If FAP is not treated the life time risk of developing a colorectal cancer is 100%. Adenocarcinomas may also develop in FAP patients. We want to present a patient with co-ocurrance of an adeocarcinoma and a neuroendocrine tumor, who had FAP syndrome and was operated in our clinic for acute mechanic intestinal obstruction. This is the first case in the literature, who was presented with co-occurance of two different tumors, without any liver metastases.