Fahr\'s syndrome is caused by calcium and phosphorus metabolism disorders, is a rare disease, characterized by bilateral symmetrical intracranial calcification and neurodegenerative disorders. The etiology is uncertain. Clinically, it is usually start with unsteadiness, slurred speech, involuntary movements and muscle cramps. Psychosis, neuropsychiatric symptoms such as personality changes can be added. In this article, we described a patient brought to emergency room with tonic-clonic seizures. He had diagnosed of epilepsy by neurology clinic before applying us. We diagnosed Fahr syndrome due to idiopathic hypoparathyroidism with diffuse bilateral basal ganglia calcification on computed tomography.